Congenital Duodenal Obstruction and Double-Bubble Sign on X-Ray

A girl weighing 1080 g was born at a gestational age of 29 weeks because of spontaneous premature rupture of membranes. Enteral feeding through a nasogastric tube was started 8 hours after birth but was not tolerated.

The infant’s condition deteriorated, with ongoing episodes of nonbilious vomiting and a lack of stools since birth. The physical examination showed mild upper abdominal distention, with apparent discomfort on abdominal palpation.

Abdominal radiography showed the double-bubble sign — a distended stomach (arrow) and proximal duodenum (arrowhead) — which is pathognomonic of congenital duodenal obstruction. There was no air distal to the level of obstruction in the D2 segment of the duodenum.

Congenital Duodenal Obstruction and Double-Bubble Sign on X-Ray
Congenital Duodenal Obstruction and Double-Bubble Sign on X-Ray

Laparoscopy showed duodenal atresia type 1, which was repaired with a diamond-shaped duodenal anastomosis. Oral feedings were initiated successfully on the seventh postoperative day. The postoperative period was uneventful.